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Crouzon’s Syndrome: Congenital craniosynostosis characterised by the premature in-utero closure of the coronal, sagittal, and lambdoid sutures. It produces an abnormal growth of the cranium, hypoplasia of the jaw, and facial asimmetry. The case of a five year old girl with Crouzon Syndrome is presented; she consulted the service of Paediatric Dentistry at School of Dentistry of Universidad del Valle (Cali,Colombia). 

This work highlights the multidisciplinary approach and the orthopaedic pre-surgical management performed, it involved an intraoral fixed device for controlled expansion with a Hyrax type screw and a facial mask for maxillary protraction as treatment before surgery. The surgery was performed in mono-block and advancement with an osteogenic distactor was done.

Key words: Crouzon syndrome, craniosynostosis, proptosis, facial Asymmetry

Paola-Andrea Díaz, Escuela de Odontología,Universidad del Valle. Cali, Colombia.

Odontóloga, Especialista en Odontología Pediátrica y Ortopedia Maxilar

Jesús-Alberto Hernández, Universidad del Valle. Cali, Colombia.

odontólogo, Especialista en Odontología Integral del Niño y Ortopedia Maxilar, Profesor titular

Díaz, P.-A., & Hernández, J.-A. (2017). Crouzon’s Syndrome: Review of the literature and case report. Revista Estomatología, 24(2).
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